Subject: Clinical medicine
Year: 2023
Type: Article
Type: PeerReviewed
Title: Perioperative anesthetic management in a child with Beckwith-Wiedman syndrome
Author: Demjanski, Vasko
Author: Mikjunovik, L
Author: Litajkovska, S
Author: Ristov, M
Author: Koskarov, K
Author: Cepreganova Cangovska, Tatjana
Abstract: Beckwith-Wiedemann Syndrome (BWS), a rare genetic disorder, poses distinctive challenges for anesthesiologists due to its associated physical anomalies and potential complications. This case report details the anesthetic management of a 2-year-old boy with BWS undergoing a procedure for agenesis testis bilateral. Key considerations include macrosomia, hypoglycemia risk, airway abnormalities, cardiovascular anomalies, and abdominal wall defects. The patient successful perioperative care involved meticulous preoperative assessment, careful planning, and collaboration with specialized medical teams. Anesthesia comprised a combination of medications, monitoring, and airway management techniques tailored to the patient’s unique needs. The discussion emphasizes the importance of considering macrosomia, hypoglycemia, anatomical abnormalities, and other factors in anesthesia planning for BWS patients. Vigilant postoperative monitoring is highlighted. The conclusion underscores the necessity for experienced anesthesiologists familiar with the challenges associated with BWS, emphasizing the significance of tailored approaches, comprehensive assessments, and collaborative care for the safety and well-being of these patients during surgical interventions.
Publisher: Department of Anaesthesia and Reanimation, Faculty of Medicine, “Ss. Cyril and Methodius” University, Skopje, Macedonia
Relation: https://eprints.ugd.edu.mk/38825/
Identifier: oai:eprints.ugd.edu.mk:38825
Identifier: https://eprints.ugd.edu.mk/38825/1/Spisanie_07-3%20%282%29.pdfIdentifier: Demjanski, Vasko and Mikjunovik, L and Litajkovska, S and Ristov, M and Koskarov, K and Cepreganova Cangovska, Tatjana (2023) Perioperative anesthetic management in a child with Beckwith-Wiedman syndrome. Macedonian Journal of Anaesthesia, 7 (3). pp. 78-80. ISSN 2545-4366
